IgG4-LINKED SYSTEMIC DISEASE. MODERN OUTLOOK ON «OLD» DISEASE

Otologic Manifestation in IgG4-Related Systemic Disease

IgG4-related systemic disease, including autoimmune pancreatitis, is a multi-organ disorder characterized by elevated serum immunoglobulin G4 (IgG4) concentration and IgG4-positive plasma cell infiltration. We report a case of a 66-year-old woman with IgG4-related hearing disorder, presenting with fluctuating mixed hearing loss with middle ear effusion. The serum IgG4 level was elevated and pat...

Recurrent pleuritis: consider IgG4-related systemic disease.

IgG4 syndrome: old disease, new perspective.

Renal manifestations of IgG4-related systemic disease

While autoimmune pancreatitis (AIP) has been recognized since the first description by Sarles et al in 1961, its involvement of other organs has been recognized more recently. Now, some form of IgG4-related systemic disease (IgG4-RSD) has been described in nearly every organ system, including the liver, gallbladder, other gastrointestinal sites, kidney, salivary and lacrimal glands, orbit, brea...

Ormond's Disease--IgG4-related Disease.

Ormond's disease is a relatively rare disease with unclear etiology, characterized by chronic periaortitis and retroperitoneal fibrosis. The inflammatory process affects the infrarenal part of the abdominal aorta and the iliac arteries, and the presence of infiltrates encasing the ureters and inferior vena cava. This disease is currently classed as an IgG4-related disease. In our review we anal...